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The assessment of food-related problems in individuals with Prader-Willi syndrome
- Authors:
- RUSSELL Helen, OLIVER Chris
- Journal article citation:
- British Journal of Clinical Psychology, 42(4), November 2003, pp.379-392.
- Publisher:
- Wiley
The objective of this study was to develop an informant-based questionnaire to assess food-related problems in people with Prader-Willi syndrome and to conduct an examination of psychometric properties. Following a content analysis of informant interview responses a 16-item questionnaire, the Food Related Problem Questionnaire (FRPQ), with three subscales (preoccupation with food, impairment of satiety and other food-related 'challenging' behaviour) was developed. Test-retest and inter-rater reliability, concurrent and criterion validity and internal consistency were examined. Total score test-retest and inter-rater reliability coefficients were both .86. Subscale test-retest and inter-rater reliability are acceptable for the subscales (range .67 to .85). Total scores on the FRPQ and all subscale scores and differentiated between a group of individuals with Prader-Willi syndrome and a comparison group (p<.001 in all cases). For relevant items of the FRPQ significant positive correlations with items on the Checklist of Challenging Behaviour were achieved. Internal consistency for the total scale was good (Cronbach's Alpha = .87). The FRPQ has sufficiently robust psychometric properties for use in future research and clinical practice to appraise the food-related problems often seen in individuals with Prader-Willi syndrome.
Social competence in persons with Prader-Willi, Williams and Down's Syndromes
- Authors:
- RISNER Beth A., et al
- Journal article citation:
- Journal of Applied Research in Intellectual Disabilities, 17(3), September 2004, pp.209-217.
- Publisher:
- Wiley
This study explores everyday social competence in the lives of persons with three genetic intellectual disability syndromes. Using parent reports on the Social and Activity Competence domains of Achenbach's Child Behavior Checklist (CBCL), socially competent behaviours were examined in 58 persons with Williams syndrome, 54 persons with Prader-Willi syndrome, and 65 persons with Down's syndrome. The Down's syndrome group showed the highest overall social competence scores, while individuals with Prader-Willi syndrome fared worst in terms of their behaviour with others. The Williams syndrome group scored lowest in terms of skill with jobs and chores, and the Down's syndrome group showed the least skill in non-sport activities. Regarding specific activities, musical activities were popular in both Williams syndrome and Down's syndrome, but more participants with Williams syndrome played musical instruments. Compared with the other groups, individuals with Prader-Willi syndrome were five to 25 times more likely to play with jigsaw puzzles, and those with Williams syndrome were least likely to engage in any visual–spatial leisure activities. Age was found to be a positive correlate of social competence for the Williams and Down's syndrome groups, but not for the Prader-Willi group. Implications are discussed for interventions and for future behavioural phenotype work