Search results for ‘Subject term:"prader-willi syndrome"’ Sort:
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Exploring patterns of unwanted behaviours in adults with Prader–Willi syndrome
- Authors:
- PIGNATTI Riccardo, et al
- Journal article citation:
- Journal of Applied Research in Intellectual Disabilities, 26(6), 2013, pp.568-577.
- Publisher:
- Wiley
Obsessive-compulsive (O-C) traits, and excessive food intake are well known behavioural manifestations among individuals with Prader–Willi Syndrome (PWS). Other unwanted behaviours are also frequently observed, but they need a more specific investigation, especially in the adult population. The behaviour of 31 PWS adults was investigated via the Symptom Checklist-90-Revised (SCL-90-R), the Yale-Brown Obsessive Compulsive Scale Symptom Checklist (Y-BOCS-SC), and the Prader–Willi Behavioural Checklist (PBC). The PBC is a quick screening questionnaire prompted specifically for the investigation on adults with PWS. Statistical clustering revealed two patterns of unwanted behaviours from the PBC. Behaviours belonging to the first cluster (e.g. Excessive food intake, Skin picking) appear to be linked to the usual phenotypic manifestation of PWS. By contrast, many other behaviours (e.g. some O-C symptoms and aggressive actions) could show a relationship also to individual psychopathologies. Both internal (Anxiety and Depression) and external (Hostility) difficulties in managing impulses should account for individually distinct behaviours in adults with PWS. (Edited publisher abstract)
Prader—Willi syndrome compulsive and ritualistic behaviours: the first population-based survey
- Authors:
- CLARKE D.J., et al
- Journal article citation:
- British Journal of Psychiatry, 180, April 2002, pp.358-362.
- Publisher:
- Cambridge University Press
Obsessive-compulsive disorder has been reported in association with Prader-Willi syndrome. This study reports the nature and prevalence of compulsive and similar symptoms associated with Prader-Willi syndrome in a population ascertained as completely as possible The results suggest that ritualistic and compulsive behaviours occur more frequently in association with Prader-Willi syndrome than among people with intellectual disability and significant obesity.